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產品詳情
  • 產品名稱:Anti-Nance-Horan Syndrome Protein抗體

  • 產品型號:南斯-霍蘭綜合征蛋白抗體
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-Nance-Horan Syndrome Protein抗體產品質量穩定,實驗效果明顯,貨期快,價格優惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-Nance-Horan Syndrome Protein抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-Nance-Horan Syndrome Protein
Cat. Number:
Anti-Nance-Horan Syndrome Protein抗體KL-19007R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
This gene encodes a protein containing four conserved nuclear localization signals. The encoded protein functions in eye, tooth, craniofacial and brain development, and it can regulate actin remodeling and cell morphology. Anti-Nance-Horan Syndrome Protein抗體Mutations in this gene have been shown to cause Nance-Horan syndrome, and also X-linked cataract-40. Alternatively spliced transcript variants encoding different isoforms have been described for this gene. [provided by RefSeq, May 2014]
Also known as:
Congenital cataracts and dental Anti-Nance-Horan Syndrome Protein抗體anomalies protein; CXN; Nance-Horan syndrome protein; nhs; NHS_HUMAN; RP3-389A20.6; SCML1.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Anti-Nance-Horan Syndrome Protein抗體Chicken, Dog, Pig, Cow, Horse, Rabbit, Sheep, .
Immunogen: KLH conjugated synthetic peptide derived from human Nance-Horan Syndrome Protein.
Predicted Molecular Weight: 179kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. Anti-Nance-Horan Syndrome Protein抗體
Optimal working dilutions must be determined by the end user.

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