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產品詳情
  • 產品名稱:Anti-GNPTAB抗體

  • 產品型號:溶酶體累積病相關蛋白/口吃相關蛋白抗體
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-GNPTAB抗體產品質量穩定,實驗效果明顯,貨期快,價格優惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-GNPTAB抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-GNPTAB
Cat. Number:
Anti-GNPTAB抗體KL-13476R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
This gene encodes two of three subunit types of the membrane-bound enzyme N-acetylglucosamine-1-phosphotransferase, a heterohexameric complex composed of two alpha, two beta, and two gamma subunits. The encoded protein is proteolytically cleaved at the Lys928-Asp929 bond to yield mature alpha and beta polypeptides while the gamma subunits are the product of a distinct gene (GeneID 84572). In the Golgi Anti-GNPTAB抗體apparatus, the heterohexameric complex catalyzes the first step in the synthesis of mannose 6-phosphate recognition markers on certain oligosaccharides of newly synthesized lysosomal enzymes. These recognition markers are essential for appropriate trafficking of lysosomal enzymes. Mutations in this gene have been associated with both mucolipidosis II and mucolipidosis IIIA.[provided by RefSeq, May 2010].
Also known as:
N-acetylglucosamine-1-phosphotransferase Anti-GNPTAB抗體subunit beta; EC=2.7.8.17; GlcNAc-1-phosphotransferase subunits alpha/beta; GNPTA; GNPTA_HUMAN; Gnptab; KIAA1208; Stealth protein GNPTAB; UDP-N-acetylglucosamine-1-phosphotransferase subunits alpha/beta.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Sheep, .
Immunogen: KLH conjugated synthetic peptide derived from human N-acetyl.
Predicted Molecular Weight: 39kDa.Anti-GNPTAB抗體
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. Anti-GNPTAB抗體
Optimal working dilutions must be determined by the end user.
kl391Hu52 肌動蛋白γ1(ACTγ1)多克隆抗體 Polyclonal Antibody to Actin Gamma 1 (ACTg1)
kl391Mu52 肌動蛋白γ1(ACTγ1)多克隆抗體 Polyclonal Antibody to Actin Gamma 1 (ACTg1)
kl391Ra51 肌動蛋白γ1(ACTγ1)多克隆抗體 Polyclonal Antibody to Actin Gamma 1 (ACTg1)
kl341Hu51 心肌肌動蛋白α1(ACTC1)多克隆抗體 Polyclonal Antibody to Actin Alpha 1, Cardiac Muscle (ACTC1)
kl341Mu51 心肌肌動蛋白α1(ACTC1)多克隆抗體 Polyclonal Antibody to Actin Alpha 1, Cardiac Muscle (ACTC1)
kl341Ra51 心肌肌動蛋白α1(ACTC1)多克隆抗體 Polyclonal Antibody to Actin Alpha 1, Cardiac Muscle (ACTC1)
kl119Hu01 金屬硫蛋白1(MT1)多克隆抗體 Polyclonal Antibody to Metallothionein 1 (MT1)
kl119Mu01 金屬硫蛋白1(MT1)多克隆抗體 Polyclonal Antibody to Metallothionein 1 (MT1)
kl119Ra01 金屬硫蛋白1(MT1)多克隆抗體 Polyclonal Antibody to Metallothionein 1 (MT1)
kl119Rb52 金屬硫蛋白1(MT1)多克隆抗體 Polyclonal Antibody to Metallothionein 1 (MT1)
kl868Hu01 金屬硫蛋白2(MT2)多克隆抗體 Polyclonal Antibody to Metallothionein 2 (MT2)
kl868Mu01 金屬硫蛋白2(MT2)多克隆抗體 Polyclonal Antibody to Metallothionein 2 (MT2)
kl868Ra01 金屬硫蛋白2(MT2)多克隆抗體 Polyclonal Antibody to Metallothionein 2 (MT2)
kl868Rb52 金屬硫蛋白2(MT2)多克隆抗體 Polyclonal Antibody to Metallothionein 2 (MT2)
kl339Hu01 肌鈣蛋白C(TNC)多克隆抗體 Polyclonal Antibody to Troponin C (TNC)
kl339Ra01 肌鈣蛋白C(TNC)多克隆抗體 Polyclonal Antibody to Troponin C (TNC)
kl339Mu01 肌鈣蛋白C(TNC)多克隆抗體 Polyclonal Antibody to Troponin C (TNC)
kl539Hu52 髓鞘堿性蛋白(MBP)多克隆抗體 Polyclonal Antibody to Myelin Basic Protein (MBP)
kl539Mu52 髓鞘堿性蛋白(MBP)多克隆抗體 Polyclonal Antibody to Myelin Basic Protein (MBP)
kl539Ra52 髓鞘堿性蛋白(MBP)多克隆抗體 Polyclonal Antibody to Myelin Basic Protein (MBP)

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