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產品詳情
  • 產品名稱:Anti-GCS1抗體

  • 產品型號:β-葡萄糖苷酶1抗體
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-GCS1抗體產品質量穩定,實驗效果明顯,貨期快,價格優惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-GCS1抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-GCS1
Cat. Number:
Anti-GCS1抗體KL-13322R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Glycosylation of asparagine residues in Asn-X-Ser/Thr motifs in proteins commonly occur in the lumen of the endoplasmicAnti-GCS1抗體 reticulum (ER). Glucosidase I catalyzes the first step in the N-linked oligosaccharide processing pathway. It specifically removes the distal alpha 1,2-linked glucose residue from the Glc3-Man9-GlcNAc2 oligosaccharide precursor. Glucosidase I contains a short cytosolic tail, a single pass transmembrane domain and a large C-terminal catalytic domain located on the luminal side of the ER. Mutations in the gene encoding Glucosidase I result in the congenital disorder glycosylation (CDG-IIb), which is characterized by generalized hypotonia, dysmorphic features, hepatomegaly, hypoventilation, feeding problems, seizures and death. Two point mutations in the Glucosidase I gene have been identified and result in amino acid substitutions, namely Arg486Thr and Phe652Leu, that affect polypeptide folding and active site formation.
Also known as:
EC 3.2.1.106; glucosidase I; Mannosyl oligosaccharide glucosidase; Mannosyl-oligosaccharide glucosidase; Mogs; MOGS_HUMAN;Anti-GCS1抗體Processing A glucosidase I; Processing A-glucosidase I.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Dog, .
Immunogen: KLH conjugated synthetic peptide derived from human GCS1.
Predicted Molecular Weight: 92kDa.Anti-GCS1抗體
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. Anti-GCS1抗體
Optimal working dilutions must be determined by the end user.
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kl406Ra01 性別決定區Y框蛋白2(SOX2)多克隆抗體 Polyclonal Antibody to Sex Determining Region Y Box Protein 2 (SOX2)
kl408Hu01 激肽釋放酶9(KLK9)多克隆抗體 Polyclonal Antibody to Kallikrein 9 (KLK9)
kl408Ra01 激肽釋放酶9(KLK9)多克隆抗體 Polyclonal Antibody to Kallikrein 9 (KLK9)
kl410Hu01 GATA結合蛋白3(GATA3)多克隆抗體 Polyclonal Antibody to GATA Binding Protein 3 (GATA3)
kl411Hu01 鈣非依賴性磷脂酶A2(iPLA2)多克隆抗體 Polyclonal Antibody to Phospholikle A2, Calcium Independent (iPLA2)
kl411Mu01 鈣非依賴性磷脂酶A2(iPLA2)多克隆抗體 Polyclonal Antibody to Phospholikle A2, Calcium Independent (iPLA2)
kl411Ra01 鈣非依賴性磷脂酶A2(iPLA2)多克隆抗體 Polyclonal Antibody to Phospholikle A2, Calcium Independent (iPLA2)
kl412Hu01 α-血紅蛋白穩定蛋白(αHSP)多克隆抗體 Polyclonal Antibody to Alpha-Hemoglobin Stabilizing Protein (aHSP)
kl414Hu01 性別決定區Y框蛋白18(SOX18)多克隆抗體 Polyclonal Antibody to Sex Determining Region Y Box Protein 18 (SOX18)
kl415Hu01 彈性蛋白微原纖維界面因子1(EMILIN1)多克隆抗體 Polyclonal Antibody to Elastin Microfibril Interface Located Protein 1 (EMILIN1)
kl416Hu01 早期生長應答因子1(EGR1)多克隆抗體 Polyclonal Antibody to Early Growth Response Protein 1 (EGR1)
kl416Mu01 早期生長應答因子1(EGR1)多克隆抗體 Polyclonal Antibody to Early Growth Response Protein 1 (EGR1)
kl419Ra01 蛋白激酶Cγ(PKCγ)多克隆抗體 Polyclonal Antibody to Protein Kinase C Gamma (PKCg)
kl422Hu01 髓鞘關聯糖蛋白(MAG)多克隆抗體 Polyclonal Antibody to Myelin Associated Glycoprotein (MAG)
kl422Ra01 髓鞘關聯糖蛋白(MAG)多克隆抗體 Polyclonal Antibody to Myelin Associated Glycoprotein (MAG)
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