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產品詳情
  • 產品名稱:Anti-GBA抗體

  • 產品型號:β-葡萄糖腦苷脂酶抗體
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-GBA抗體產品質量穩定,實驗效果明顯,貨期快,價格優惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-GBA抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-GBA
Cat. Number:
Anti-GBA抗體KL-11779R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
This gene encodes a lysosomal membrane protein that cleaves the beta-glucosidic linkage of glycosylceramide, an intermediate in glycolipid metabolism. Mutations in this gene cause Gaucher disease, a lysosomal storage disease Anti-GBA抗體characterized by an accumulation of glucocerebrosides. A related pseudogene is approximately 12 kb downstream of this gene on chromosome 1. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jan 2010]
Also known as:
Glucosidase beta; Acid beta Anti-GBA抗體glucosidase; Acid beta-glucosidase; Alglucerase; Beta glucocerebrosidase; BETA GLUCOSIDASE, ACID; Beta-glucocerebrosidase; betaGC; D glucosyl N acylsphingosine glucohydrolase; D-glucosyl-N-acylsphingosine glucohydrolase; EC 3.2.1.45 ; GBA; Gba protein; GBA1; GC antibody GCase; GCB; GLCM_HUMAN; GLUC; Glucocerebrosidase (alt.); Glucocerebrosidase; GLUCOCEREBROSIDASE PSEUDOGENE; Glucosidase beta; Glucosidase, beta, acid; Glucosidase, beta; acid (includes glucosylceramidase); Glucosylceramidase; Imiglucerase; Lysosomal glucocerebrosidase.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Rabbit, .Anti-GBA抗體
Immunogen: KLH conjugated synthetic peptide derived from human Glucosid.
Predicted Molecular Weight: 56kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   Anti-GBA抗體
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.
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kl070Hu01 趨化因子C-基元配體2(XCL2)多克隆抗體 Polyclonal Antibody to Chemokine C-Motif Ligand 2 (XCL2)
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kl076Hu01 層粘連蛋白α3(LAMα3)多克隆抗體 Polyclonal Antibody to Laminin Alpha 3 (LAMa3)
kl077Hu01 層粘連蛋白α4(LAMα4)多克隆抗體 Polyclonal Antibody to Laminin Alpha 4 (LAMa4)
kl078Hu01 層粘連蛋白α5(LAMα5)多克隆抗體 Polyclonal Antibody to Laminin Alpha 5 (LAMa5)
kl080Hu01 層粘連蛋白β2(LAMβ2)多克隆抗體 Polyclonal Antibody to Laminin Beta 2 (LAMb2)
kl081Hu01 層粘連蛋白β3(LAMβ3)多克隆抗體 Polyclonal Antibody to Laminin Beta 3 (LAMb3)
kl083Hu01 層粘連蛋白γ2(LAMγ2)多克隆抗體 Polyclonal Antibody to Laminin Gamma 2 (LAMC2)
kl086Hu01 Ⅰ類主要組織相容性復合體C(MHCC)多克隆抗體 Polyclonal Antibody to Major Histocomklibility Complex Class I C (MHCC)
kl097Hu01 整合素α11(ITGα11)多克隆抗體 Polyclonal Antibody to Integrin Alpha 11 (ITGa11)
kl099Hu01 整合素β6(ITGβ6)多克隆抗體 Polyclonal Antibody to Integrin Beta 6 (ITGb6)
kl102Hu01 骨成型蛋白3(BMP3)多克隆抗體 Polyclonal Antibody to Bone Morphogenetic Protein 3 (BMP3)
kl105Mu01 骨形成蛋白8B(BMP8B)多克隆抗體 Polyclonal Antibody to Bone Morphogenetic Protein 8B (BMP8B)
kl106Hu01 骨成型蛋白10(BMP10)多克隆抗體 Polyclonal Antibody to Bone Morphogenetic Protein 10 (BMP10)
kl106Mu01 骨成型蛋白10(BMP10)多克隆抗體 Polyclonal Antibody to Bone Morphogenetic Protein 10 (BMP10)
kl107Hu01 骨形成蛋白15(BMP15)多克隆抗體 Polyclonal Antibody to Bone Morphogenetic Protein 15 (BMP15)
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kl109Mu01 生長分化因子3(GDF3)多克隆抗體 Polyclonal Antibody to Growth Differentiation Factor 3 (GDF3)
kl109Ra01 生長分化因子3(GDF3)多克隆抗體 Polyclonal Antibody to Growth Differentiation Factor 3 (GDF3)

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