產品詳情
簡單介紹：
Anti-GBE1抗體產品質量穩定，實驗效果明顯，貨期快，價格優惠，歡迎垂詢訂購！我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-GBE1抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹：
Rabbit Anti-GBE1
Cat. Number:
Anti-GBE1抗體KL-13300R
Quantity size:
0.2ml
Concentration:
1mg/ml Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
GBE1 is a 702 amino acid protein that is expressed at high levels in muscle and liver and is involved in glycogen biosynthesis. Existing as a monomer, GBE1 catalyzes the transfer of alpha-1,4-linked glucosyl units from the outer end of a glycogen chain to an alpha-1,6 position on a neighboring glycogen Anti-GBE1抗體chain and, via this catalytic activity, plays an essential role in glycogen accumulation. Defects in the gene encoding GBE1 are the cause of glycogen storage disease type 4 (GSD4) and ***** polyglucosan body disease (APBD), the first of which is a metabolic disorder that is associated with the accumulation of polysaccharides and is characterized by liver disease during childhood. Unlike GSD4, APBD is a late-onset disorder that affects the central and peripheral nervous systems and is characterized by cognitive impairment, pyramidal tetraparesis and peripheral neuropathy.
Also known as:
1,4 alpha glucan branching Anti-GBE1抗體enzyme; 4-alpha-glucan-branching enzyme; amylo (1,4 to 1,6) transglucosidase; amylo (1,4 to 1,6) transglycosylase; Andersen disease; Brancher enzyme; GBE 1; GBE; GBE1; gGlucan (1,4 alpha ), branching enzyme 1; GLGB_HUMAN; Glucan (1,4 alpha) branching enzyme; Glycogen branching enzyme; Glycogen storage disease type IV; Glycogen-branching enzyme; OTTHUMP00000213788; OTTHUMP00000213833.
Specificity:
●
Rabbit Polyclonal IgG, affinity purified by Protein A.
●
Reacts with: Human, Mouse, Rat, Rabbit, .
●
Immunogen: KLH conjugated synthetic peptide derived from human GBE1.
●
Predicted Molecular Weight: 80kDa.
Storage:
Shipped at 4℃, Store at -20℃Anti-GBE1抗體 (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500
Not yet tested in other applications.
Optimal working dilutions Anti-GBE1抗體must be determined by the end user.
Not yet tested in other applications.
Optimal working dilutions Anti-GBE1抗體must be determined by the end user.
kl560Hu01 絲裂原激活蛋白激酶激酶7(MAP2K7)多克隆抗體 Polyclonal Antibody to Mitogen Activated Protein Kinase Kinase 7 (MAP2K7)
kl564Hu01 絲裂原激活蛋白激酶激酶4(MAP2K4)多克隆抗體 Polyclonal Antibody to Mitogen Activated Protein Kinase Kinase 4 (MAP2K4)
kl748Hu01 低密度脂蛋白受體相關蛋白3(LRP3)多克隆抗體 Polyclonal Antibody to Low Density Lipoprotein Receptor Related Protein 3 (LRP3)
kl949Hu01 RAR相關孤兒素受體γ(RORγ)多克隆抗體 Polyclonal Antibody to RAR Related Orphan Receptor Gamma (RORg)
kl110Mu01 肝配蛋白A4(EFNA4)多克隆抗體 Polyclonal Antibody to Ephrin A4 (EFNA4)
kl110Ra01 肝配蛋白A4(EFNA4)多克隆抗體 Polyclonal Antibody to Ephrin A4 (EFNA4)
kl110Ra02 肝配蛋白A4(EFNA4)多克隆抗體 Polyclonal Antibody to Ephrin A4 (EFNA4)
kl958Hu01 丙酮酸脫氫酶激酶同工酶4(PDK4)多克隆抗體 Polyclonal Antibody to Pyruvate Dehydrogenase Kinase Isozyme 4 (PDK4)
kl436Mu01 含DIX域蛋白1(DIXDC1)多克隆抗體 Polyclonal Antibody to DIX Domain Containing Protein 1 (DIXDC1)
kl285Mu01 整合素α6(ITGα6)多克隆抗體 Polyclonal Antibody to Integrin Alpha 6 (ITGa6)
kl042Mu01 整合素β1(ITGβ1)多克隆抗體 Polyclonal Antibody to Integrin Beta 1 (ITGb1)
kl586Mu01 整合素β2(ITGβ2)多克隆抗體 Polyclonal Antibody to Integrin Beta 2 (ITGb2)
kl718Mu01 丙酮酸脫氫酶激酶同工酶1(PDK1)多克隆抗體 Polyclonal Antibody to Pyruvate Dehydrogenase Kinase Isozyme 1 (PDK1)
kl464Mu01 丙酮酸脫氫酶激酶同工酶2(PDK2)多克隆抗體 Polyclonal Antibody to Pyruvate Dehydrogenase Kinase Isozyme 2 (PDK2)
kl531Mu01 含FYVE指磷酸肌醇激酶(PIKFYVE)多克隆抗體 Polyclonal Antibody to Phosphoinositide Kinase, FYVE Finger Containing (PIKFYVE)
kl797Mu01 Pim-2原癌基因(PIM2)多克隆抗體 Polyclonal Antibody to Pim-2 Oncogene (PIM2)
kl057Mu01 PTEN誘導假定激酶1(PINK1)多克隆抗體 Polyclonal Antibody to PTEN Induced Putative Kinase 1 (PINK1)
kl805Mu01 腫瘤壞死因子α誘導蛋白3相互作用蛋白2(TNIP2)多克隆抗體 Polyclonal Antibody to Tumor Necrosis Factor Alpha Induced Protein 3 Interacting Protein 2 (TNIP2)
