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產(chǎn)品詳情
  • 產(chǎn)品名稱:Anti-BBS4抗體

  • 產(chǎn)品型號:巴爾得-別德爾綜合征相關(guān)蛋白4抗體
  • 產(chǎn)品廠商:KALANG
  • 產(chǎn)品文檔:
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簡單介紹:
Anti-BBS4抗體產(chǎn)品質(zhì)量穩(wěn)定,實驗效果明顯,貨期快,價格優(yōu)惠,歡迎垂詢訂購!我公司長期供應(yīng)**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關(guān)試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-BBS4抗體用于**組化實驗,WB實驗,相應(yīng)的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-BBS4
Cat. Number:
Anti-BBS4抗體KL-11508R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Bardet-Biedl syndrome Anti-BBS4抗體(BBS) is a pleiotropic genetic disorder characterized by obesity, photoreceptor degeneration, polydactyly, hypogenitalism, renal abnormalities, and developmental delay. Other associated clinical findings in BBS patients include diabetes, hypertension, and congenital heart defects. BBS is a heterogeneous disorder; BBS genes map to eight genetic loci and encode eight proteins, BBS1-BBS8. Five BBS genes encode basal body or cilia proteins, suggesting that BBS is a ciliary dysfunction disorder. BBS4 is expressed in the olfactory epithelium and localizes to the centriolar satellites of centrosomes and basal bodies of primary cilia. BBS4 regulates the p150 subunit of the dynein transport machinery (DCTN1) to attract pericentriolar material-1 protein (PCM1) and its associated components to the satellites. Loss of BBS4 is correlated with obesity caused by abnormal lipid profiles, liver dysfunction, elevated insulin, and abnormal leptin levels.Anti-BBS4抗體
Also known as:
Bardet Biedl syndrome 4 protein; Bardet-Biedl syndrome 4 protein; Bbs4; BBS4_HUMAN.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.Anti-BBS4抗體
Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Horse, Sheep, .
Immunogen: KLH conjugated synthetic peptide derived from human BBS4.
Predicted Molecular Weight: 58kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions Anti-BBS4抗體must be determined by the end user.
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kl480Po01 肌紅蛋白(MYO)多克隆抗體 Polyclonal Antibody to Myoglobin (MYO)
kl483Hu01 內(nèi)皮素轉(zhuǎn)化酶1(ECE1)多克隆抗體 Polyclonal Antibody to Endothelin Converting Enzyme 1 (ECE1)
kl483Mu01 內(nèi)皮素轉(zhuǎn)化酶1(ECE1)多克隆抗體 Polyclonal Antibody to Endothelin Converting Enzyme 1 (ECE1)
kl484Hu01 氨基端前心鈉肽(NT-ProANP)多克隆抗體 Polyclonal Antibody to N-Terminal Pro-Atrial Natriuretic Peptide (NT-ProANP)
kl484Mu01 氨基端前心鈉肽(NT-ProANP)多克隆抗體 Polyclonal Antibody to N-Terminal Pro-Atrial Natriuretic Peptide (NT-ProANP)
kl484Ra01 氨基端前心鈉肽(NT-ProANP)多克隆抗體 Polyclonal Antibody to N-Terminal Pro-Atrial Natriuretic Peptide (NT-ProANP)
kl488Hu01 角蛋白5(KRT5)多克隆抗體 Polyclonal Antibody to Keratin 5 (KRT5)
kl489Hu01 角蛋白4(KRT4)多克隆抗體 Polyclonal Antibody to Keratin 4 (KRT4)
kl491Hu01 角蛋白2(KRT2)多克隆抗體 Polyclonal Antibody to Keratin 2 (KRT2)
kl492Hu01 角蛋白1(KRT1)多克隆抗體 Polyclonal Antibody to Keratin 1 (KRT1)
kl500Hu01 嵌套蛋白(NES)多克隆抗體 Polyclonal Antibody to Nestin (NES)
kl512Hu01 纖維介素蛋白(FGL2)多克隆抗體 Polyclonal Antibody to Fibrinogen Like Protein 2 (FGL2)
kl512Mu01 纖維介素蛋白(FGL2)多克隆抗體 Polyclonal Antibody to Fibrinogen Like Protein 2 (FGL2)
kl514Hu01 失調(diào)蛋白1(ATXN1)多克隆抗體 Polyclonal Antibody to Ataxin 1 (ATXN1)
kl516Hu01 角蛋白16(KRT16)多克隆抗體 Polyclonal Antibody to Keratin 16 (KRT16)
kl517Hu01 角蛋白15(KRT15)多克隆抗體 Polyclonal Antibody to Keratin 15 (KRT15)
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kl522Hu01 角蛋白14(KRT14)多克隆抗體 Polyclonal Antibody to Keratin 14 (KRT14)

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