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產品詳情
  • 產品名稱:Anti-BBS5抗體

  • 產品型號:巴德-畢德氏綜合征蛋白BBS5抗體
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-BBS5抗體產品質量穩定,實驗效果明顯,貨期快,價格優惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-BBS5抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-BBS5
Cat. Number:
Anti-BBS5抗體KL-9438R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M Anti-BBS5抗體TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Bardet-Biedl syndrome (BBS) is a pleiotropic genetic disorder characterized by obesity, photoreceptor degeneration, polydactyly, hypogenitalism, renal abnormalities, and developmental delay. Other associated clinical findings in BBS patients include diabetes, hypertension and congenital heart defects. BBS is a heterogeneous disorder; BBS genes map to eight genetic loci and encode eight proteins, BBS1-BBS8. Five BBS genes encode basal body or cilia proteins, suggesting that BBS is a ciliary dysfunction disorder. BBS5 localizes to ciliary basal bodies and is a member of the basal body/flagellar proteome. It plays a role in flagellar and basal body assembly and function. A mutation or loss Anti-BBS5抗體of BBS5 may be correlated with photoreceptor degeneration
Also known as:
Bardet Biedl syndrome 5 Anti-BBS5抗體protein; BBS 5; BBS-5.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Horse, .
Immunogen: KLH conjugated synthetic peptide derived from human BBS5.
Predicted Molecular Weight: 38kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  IF=1:50-200   
Not yet tested in other applications. 
Optimal working Anti-BBS5抗體dilutions must be determined by the end user.
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kl175Hu01 干擾素α4(IFNα4)多克隆抗體 Polyclonal Antibody to Interferon Alpha 4 (IFNa4)
kl177Hu01 酸性葡糖苷酶α(GαA)多克隆抗體 Polyclonal Antibody to Glucosidase Alpha, Acid (GaA)
kl179Hu01 干擾素α2(IFNα2)多克隆抗體 Polyclonal Antibody to Interferon Alpha 2 (IFNa2)
kl181Ca01 中性粒細胞彈性蛋白酶(ELA2)多克隆抗體 Polyclonal Antibody to Elastase 2, Neutrophil (ELA2)
kl181Hu01 中性粒細胞彈性蛋白酶(ELA2)多克隆抗體 Polyclonal Antibody to Elastase 2, Neutrophil (ELA2)
kl181Mu01 中性粒細胞彈性蛋白酶(ELA2)多克隆抗體 Polyclonal Antibody to Elastase 2, Neutrophil (ELA2)
kl181Ra01 中性粒細胞彈性蛋白酶(ELA2)多克隆抗體 Polyclonal Antibody to Elastase 2, Neutrophil (ELA2)
kl183Hu01 半乳糖苷酶α(GLα)多克隆抗體 Polyclonal Antibody to Galactosidase Alpha (GLa)
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kl184Hu01 層粘連蛋白β1(LAMβ1)多克隆抗體 Polyclonal Antibody to Laminin Beta 1 (LAMb1)
kl190Hu01 糖化血紅蛋白A1c(HbA1c)多克隆抗體 Polyclonal Antibody to Glycated Hemoglobin A1c (HbA1c)
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kl193Po01 纖維蛋白原(FG)多克隆抗體 Polyclonal Antibody to Fibrinogen (FG)
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kl196Bo01 半乳糖苷酶β(GLβ)多克隆抗體 Polyclonal Antibody to Galactosidase Beta (GLb)

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