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產(chǎn)品詳情
  • 產(chǎn)品名稱:Anti-GNS抗體

  • 產(chǎn)品型號(hào):氨基葡萄糖6-硫酸酯酶抗體
  • 產(chǎn)品廠商:KALANG
  • 產(chǎn)品文檔:
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簡單介紹:
Anti-GNS抗體產(chǎn)品質(zhì)量穩(wěn)定,實(shí)驗(yàn)效果明顯,貨期快,價(jià)格優(yōu)惠,歡迎垂詢訂購!我公司長期供應(yīng)**組化抗體、WB抗體、**組化試劑盒和抗體試驗(yàn)所需全部相關(guān)試劑、熒光標(biāo)記抗體、單克隆抗體、多克隆抗體、各種標(biāo)記的二抗IgG/IgM/IgD/IgA等科研實(shí)驗(yàn)抗體。Anti-GNS抗體用于**組化實(shí)驗(yàn),WB實(shí)驗(yàn),相應(yīng)的標(biāo)記抗體有HRP標(biāo)記抗體,FITC標(biāo)記,BIO等。
詳情介紹:
Rabbit  Anti-GNS
Cat. Number:
Anti-GNS抗體KL-13479R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
GNS is a 552 amino acid lysosomal enzyme that hydrolyzes the 6-sulfate groups of the N-acetyl-D-glucosamine 6-sulfate units of keratan sulfate and heparan sulfate. A member of the sulfatase family, GNS assists in the catabolism of heparin, and binds calcium as a cofactor. GNS deficiency results in an autosomal recessive lysosomal Anti-GNS抗體storage disorder known as mucopolysaccharidosis type IIID (Sanfilippo D syndrome), which is characterized by mild somatic disease and severe degeneration of the central nervous system. Subject to post-translational internal peptidase cleavage, GNS is encoded by a gene mapping to human chromosome 12q14.2 and mouse chromosome 10 D2.
Also known as:
2610016K11Rik; AU042285; C87209; G6S; Anti-GNS抗體Glucosamine (N-acetyl) 6 sulfatase; Glucosamine 6 sulfatase; Glucosamine-6-sulfatase; GNS; GNS_HUMAN; MGC21274; N acetylglucosamine 6 sulfatase [Precursor]; N-acetylglucosamine-6-sulfatase; N28088.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Cow, Horse, Rabbit, .
Immunogen: KLH conjugated synthetic peptide derived from human GNS/Gluc.
Predicted Molecular Weight: 58kDa.Anti-GNS抗體
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. Anti-GNS抗體
Optimal working dilutions must be determined by the end user.
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kl017Po01 α2-巨球蛋白(α2M)多克隆抗體 Polyclonal Antibody to Alpha-2-Macroglobulin (a2M)
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kl519Po01 載脂蛋白A1(APOA1)多克隆抗體 Polyclonal Antibody to Apolipoprotein A1 (APOA1)
kl519Bo01 載脂蛋白A1(APOA1)多克隆抗體 Polyclonal Antibody to Apolipoprotein A1 (APOA1)
kl604Si01 載脂蛋白A2(APOA2)多克隆抗體 Polyclonal Antibody to Apolipoprotein A2 (APOA2)
kl604Po01 載脂蛋白A2(APOA2)多克隆抗體 Polyclonal Antibody to Apolipoprotein A2 (APOA2)
kl603Rb51 載脂蛋白B100(APOB100)多克隆抗體 Polyclonal Antibody to Apolipoprotein B100 (APOB100)
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