產品詳情
簡單介紹：
Anti-Galactosidase alpha抗體產品質量穩定，實驗效果明顯，貨期快，價格優惠，歡迎垂詢訂購！我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-Galactosidase alpha抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹：
Rabbit Anti-Galactosidase alpha
Cat. Number:
Anti-Galactosidase alpha抗體KL-7593R
Quantity size:
0.2ml
Concentration:
1mg/ml Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Galactosidase alpha is involved in the hydrolysis of terminal, non reducing alpha D galactose residues in alpha D galactosides, Anti-Galactosidase alpha抗體including galactose oligosaccharides, galactomannans and galactohydrolase. Defects in GLA are the cause of Fabry's disease (FD). FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. Clinical recognition in males results from characteristic skin lesions (angiokeratomas) over the lower trunk. Patients may show ocular deposits, febrile episodes, and burning pain in the extremities. Death results from renal failure, cardiac or cerebral complications of hypertension or other vascular disease. Heterozygous females may exhibit the disorder in an attenuated form, they are more likely to show corneal opacities.
Also known as:
Galactosidase alpha; Alpha D Anti-Galactosidase alpha抗體galactosidase A; Alpha D galactoside galactohydrolase; Melibiase; Alpha galactosidase A; GALA; GLA; GLA protein; AGAL_HUMAN.
Specificity:
●
Rabbit Polyclonal IgG, affinity purified by Protein A.
●
Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Rabbit, .
●
Immunogen: KLH conjugated synthetic peptide derived from human Galactos.
●
Predicted Molecular Weight: 45kDa.Anti-Galactosidase alpha抗體
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 IF=1:100-500
Not yet tested in other applications. Anti-Galactosidase alpha抗體
Optimal working dilutions must be determined by the end user.
Not yet tested in other applications. Anti-Galactosidase alpha抗體
Optimal working dilutions must be determined by the end user.
kl035Hu01 成纖維細胞生長因子6(FGF6)多克隆抗體 Polyclonal Antibody to Fibroblast Growth Factor 6 (FGF6)
kl035Mu01 成纖維細胞生長因子6(FGF6)多克隆抗體 Polyclonal Antibody to Fibroblast Growth Factor 6 (FGF6)
kl035Ra01 成纖維細胞生長因子6(FGF6)多克隆抗體 Polyclonal Antibody to Fibroblast Growth Factor 6 (FGF6)
kl036Ga01 成纖維細胞生長因子9(FGF9)多克隆抗體 Polyclonal Antibody to Fibroblast Growth Factor 9 (FGF9)
kl036Hu01 成纖維細胞生長因子9(FGF9)多克隆抗體 Polyclonal Antibody to Fibroblast Growth Factor 9 (FGF9)
kl036Mu01 成纖維細胞生長因子9(FGF9)多克隆抗體 Polyclonal Antibody to Fibroblast Growth Factor 9 (FGF9)
kl036Po01 成纖維細胞生長因子9(FGF9)多克隆抗體 Polyclonal Antibody to Fibroblast Growth Factor 9 (FGF9)
kl036Ra01 成纖維細胞生長因子9(FGF9)多克隆抗體 Polyclonal Antibody to Fibroblast Growth Factor 9 (FGF9)
kl038Hu01 FMS樣酪氨酸激酶3配體(Flt3L)多克隆抗體 Polyclonal Antibody to FMS Like Tyrosine Kinase 3 Ligand (Flt3L)
kl038Mu01 FMS樣酪氨酸激酶3配體(Flt3L)多克隆抗體 Polyclonal Antibody to FMS Like Tyrosine Kinase 3 Ligand (Flt3L)
kl039Hu01 FMS樣酪氨酸激酶3(Flt3)多克隆抗體 Polyclonal Antibody to FMS Like Tyrosine Kinase 3 (Flt3)
kl040Hu01 趨化因子C-X3-C-基元配體1(CX3CL1)多克隆抗體 Polyclonal Antibody to Chemokine C-X3-C-Motif Ligand 1 (CX3CL1)
kl040Mu01 趨化因子C-X3-C-基元配體1(CX3CL1)多克隆抗體 Polyclonal Antibody to Chemokine C-X3-C-Motif Ligand 1 (CX3CL1)
kl040Ra01 趨化因子C-X3-C-基元配體1(CX3CL1)多克隆抗體 Polyclonal Antibody to Chemokine C-X3-C-Motif Ligand 1 (CX3CL1)
kl041Hu01 中性粒細胞激活蛋白3(NAP3)多克隆抗體 Polyclonal Antibody to Neutrophil Activating Protein 3 (NAP3)
kl041Mu01 中性粒細胞激活蛋白3(NAP3)多克隆抗體 Polyclonal Antibody to Neutrophil Activating Protein 3 (NAP3)
