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產品詳情
  • 產品名稱:Anti-Fumarate hydratase抗體

  • 產品型號:富馬酸水合酶抗體
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-Fumarate hydratase抗體產品質量穩定,實驗效果明顯,貨期快,價格優惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-Fumarate hydratase抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-Fumarate hydratase
Cat. Number:
Anti-Fumarate hydratase抗體KL-3938R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Defects in FH are the cause Anti-Fumarate hydratase抗體of fumarase deficiency (FHD)also known as fumaricaciduria. FHD is characterized by progressive encephalopathy, developmental delay, hypotonia, cerebral atrophy and lactic and pyruvic acidemia.
Also known as:
mitochondrial; FH; Fumarase; Fumarate hydratase; Fumarate hydratase mitochondrial; FUMH_HUMAN; HLRCC; LRCC; Anti-Fumarate hydratase抗體MCL; MCUL 1; MCUL1; Multiple hereditary cutaneous leiomyomata.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Dog, Anti-Fumarate hydratase抗體Pig, Cow, Horse, Rabbit, Sheep, .
Immunogen: KLH conjugated synthetic peptide derived from human Fumarate.
Predicted Molecular Weight: 51kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  IF=1:100-500   
Not yet tested in other applications. Anti-Fumarate hydratase抗體
Optimal working dilutions must be determined by the end user.
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