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產品詳情
  • 產品名稱:Anti-CHM抗體

  • 產品型號:遺傳性脈絡膜缺乏癥相關蛋白抗體
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-CHM抗體產品質量穩(wěn)定,實驗效果明顯,貨期快,價格優(yōu)惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-CHM抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-CHM
Cat. Number:
Anti-CHM抗體KL-13911R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
This gene encodes component A of the RAB geranylgeranyl transferase holoenzyme. In the dimeric holoenzyme, this subunit binds unprenylated Rab GTPases and then presents them to the catalytic Rab GGTase Anti-CHM抗體subunit for the geranylgeranyl transfer reaction. Rab GTPases need to be geranylgeranyled on either one or two cysteine residues in their C-terminus to localize to the correct intracellular membrane. Mutations in this gene are a cause of choroideremia; also known as tapetochoroidal dystrophy (TCD). This X-linked disease is characterized by progressive dystrophy of the choroid, retinal pigment epithelium and retina. Alternative splicing results in multiple transcript variants encoding different isoforms.[provided by RefSeq, Feb 2009]
Also known as:
CHM; Chm; Choroideraemia protein; Anti-CHM抗體Choroideremia; DXS540; FLJ38564; GGTA; HSD 32; MGC102710; Rab escort protein 1; Rab geranylgeranyltransferase component A; Rab proteins geranylgeranyltransferase component A 1; RAE1_HUMAN; REP 1; REP-1; REP1; TCD; TCD protein.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, .
Immunogen: KLH conjugated synthetic Anti-CHM抗體peptide derived from human CHM.
Predicted Molecular Weight: 73kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. Anti-CHM抗體
Optimal working dilutions must be determined by the end user.
kl084Rb51 瘦素(LEP)多克隆抗體 Polyclonal Antibody to Leptin (LEP)
kl084Ca01 瘦素(LEP)多克隆抗體 Polyclonal Antibody to Leptin (LEP)
kl084Po01 瘦素(LEP)多克隆抗體 Polyclonal Antibody to Leptin (LEP)
kl084Bo01 瘦素(LEP)多克隆抗體 Polyclonal Antibody to Leptin (LEP)
kl084Cp01 瘦素(LEP)多克隆抗體 Polyclonal Antibody to Leptin (LEP)
kl084Eq01 瘦素(LEP)多克隆抗體 Polyclonal Antibody to Leptin (LEP)
kl084Ga01 瘦素(LEP)多克隆抗體 Polyclonal Antibody to Leptin (LEP)
kl621Ge01 羥脯氨酸(Hyp)多克隆抗體 Polyclonal Antibody to Hydroxyproline (Hyp)
kl109Ge01 異亮氨酸(Ile)多克隆抗體 Polyclonal Antibody to Isoleucine (Ile)
kl110Ge01 亮氨酸(Leu)多克隆抗體 Polyclonal Antibody to Leucine (Leu)
kl466Ge01 蛋氨酸(Met)多克隆抗體 Polyclonal Antibody to Methionine (Met)
kl111Ge01 苯丙氨酸(Phe)多克隆抗體 Polyclonal Antibody to Phenylalanine (Phe)
kl780Ca01 乳鐵傳遞蛋白(LTF)多克隆抗體 Polyclonal Antibody to Lactoferrin (LTF)
kl780Po01 乳鐵傳遞蛋白(LTF)多克隆抗體 Polyclonal Antibody to Lactoferrin (LTF)
kl780Bo01 乳鐵傳遞蛋白(LTF)多克隆抗體 Polyclonal Antibody to Lactoferrin (LTF)
kl780Cp01 乳鐵傳遞蛋白(LTF)多克隆抗體 Polyclonal Antibody to Lactoferrin (LTF)
kl780Eq01 乳鐵傳遞蛋白(LTF)多克隆抗體 Polyclonal Antibody to Lactoferrin (LTF)

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