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產品詳情
  • 產品名稱:Anti-CLN8抗體

  • 產品型號:神經細胞蠟樣質脂褐質沉積病蛋白CLN8抗體
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-CLN8抗體產品質量穩定,實驗效果明顯,貨期快,價格優惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-CLN8抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-CLN8
Cat. Number:
Anti-CLN8抗體KL-11715R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
CLN8, a 286 amino acid transmembrane protein, localizes mainly to the endoplasmic reticulum, but also partially to the ER-Golgi intermediate compartment (ERGIC). Mutations in the CLN8 gene cause neuronal ceroid lipofuscinosis 8 and progressive epilepsy with mental retardation (EPMR). Both disorders are forms Anti-CLN8抗體of neuronal ceroid-lipofuscinose (NCL), a group of progressive neurodegenerative diseases found in children, characterized by failure of psychomotor development, impaired vision, seizures and premature death. The CLN8 protein is one of eight proteins in the CLN family, including CLN1-CLN7, which are associated with NCL.
Also known as:
Ceroid-lipofuscinosis, Anti-CLN8抗體neuronal 8 (epilepsy, progressive with mental retardation); Cln8; CLN8_HUMAN; EPMR; Protein CLN8.
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Dog, Pig, Horse, Rabbit, .
Immunogen: KLH conjugated synthetic peptide derived from human CLN8 (201-286aa).
Predicted Molecular Weight: 33kDa.
Storage:
Shipped at 4℃, Store Anti-CLN8抗體at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working Anti-CLN8抗體dilutions must be determined by the end user.
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kl934Hu01 Numb同源物(NUMB)多克隆抗體 Polyclonal Antibody to Numb Homolog (NUMB)
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