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產品詳情
  • 產品名稱:Anti-C2ORF47抗體

  • 產品型號:2號染色體開放閱讀框47抗體
  • 產品廠商:KALANG
  • 產品文檔:
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簡單介紹:
Anti-C2ORF47抗體產品質量穩定,實驗效果明顯,貨期快,價格優惠,歡迎垂詢訂購!我公司長期供應**組化抗體、WB抗體、**組化試劑盒和抗體試驗所需全部相關試劑、熒光標記抗體、單克隆抗體、多克隆抗體、各種標記的二抗IgG/IgM/IgD/IgA等科研實驗抗體。Anti-C2ORF47抗體用于**組化實驗,WB實驗,相應的標記抗體有HRP標記抗體,FITC標記,BIO等。
詳情介紹:
Rabbit  Anti-C2ORF47
Cat. Number:
Anti-C2ORF47抗體KL-9811R
Quantity size:
0.2ml
Concentration:
1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
C2orf47, also known as FLJ22555 or DKFZp666A212, is a 291 amino acid mitochondrial protein that is encoded by a gene located on human chromosome 2q33.1. The second largest human chromosome, chromosome 2 consists of 237 million bases, encodes over 1,400 genes and makes up approximately 8% of the human genome. A number of genetic diseases are linked to genes on chromosome 2. Harlequin icthyosis, a rare and morbid skin deformity, is associated with mutations in the ABCA12 gene. Anti-C2ORF47抗體The lipid metabolic disorder sitosterolemia is associated with ABCG5 and ABCG8. An extremely rare recessive genetic disorder, Alstr鰉 syndrome is due to mutations in the ALMS1 gene. Interestingly, chromosome 2 contains what appears to be a vestigial second centromere and vestigial telomeres which gives credence to the hypothesis that human chromosome 2 is the result of an ancient fusion of two ancestral chromosomes seen in modern form today in apes.
Also known as:
Chromosome 2 open Anti-C2ORF47抗體reading frame 47; Hhypothetical protein LOC79568;
Specificity:
Rabbit Polyclonal IgG, affinity purified by Protein A.
Reacts with: Human, Mouse, Rat, Dog, Cow, Rabbit, Sheep, .
Immunogen: KLH conjugated synthetic peptide derived from human C2ORF47.
Predicted Molecular Anti-C2ORF47抗體Weight: 22kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  IF=1:50-200  IEM=1:20-200  IGS=1:20-200  GICA=1:20-200   
Not yet tested in Anti-C2ORF47抗體other applications. 
Optimal working dilutions must be determined by the end user.
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kl593Mu01 肌原纖蛋白1(FBN1)多克隆抗體 Polyclonal Antibody to Fibrillin 1 (FBN1)

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